Congenital cysts of the larynx occur rarely. Their incidence amounts to about 1.8/100,000 newborns. Most frequently, these cysts are located in the supraglottic region, 75% of them within the plica aryepiglottica. The leading symptoms, inspiratoric stridor, cyanosis, and jugular and epigastric retractions, are caused by blockage of the airway. Therefore, laryngeal cysts often lead to severe respiratory obstruction immediately post partum, giving rise to an emergency intervention. The case report demonstrates a newborn with a laryngeal cyst located in the region of the right plica aryepiglottica. After emergency intubation, a primary punction and, some days later, a secondary endoscopic cyst removal were performed.