Abstract
This article reviews current concepts regarding the pathobiology of cystic fibrosis pancreatic disease. It summarizes recent studies on the relationship between CFTR mutations and pancreatitis, and it reviews several unresolved issues in the field.
MeSH terms
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Carrier Proteins / genetics*
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Carrier Proteins / metabolism
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Chronic Disease
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Cystic Fibrosis / epidemiology
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Cystic Fibrosis / genetics*
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Cystic Fibrosis / physiopathology
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Cystic Fibrosis Transmembrane Conductance Regulator / genetics*
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Cystic Fibrosis Transmembrane Conductance Regulator / metabolism
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Genetic Predisposition to Disease
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Humans
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Pancreatitis / epidemiology
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Pancreatitis / genetics*
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Pancreatitis / physiopathology
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Risk Factors
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Trypsin Inhibitor, Kazal Pancreatic
Substances
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CFTR protein, human
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Carrier Proteins
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SPINK1 protein, human
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Cystic Fibrosis Transmembrane Conductance Regulator
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Trypsin Inhibitor, Kazal Pancreatic