Dubowitz syndrome is a rare condition in which the affected individual presents with dysmorphic facial features and manifests growth retardation. Although the condition is well reported in the medical literature, the dental manifestations have not been discussed in great detail. Some of the dental features reported include macrodontia, hypodontia, delayed eruption, and midline diastema. The purpose of this case report was to describe a young Chinese patient with Dubowitz syndrome with specific oral features.