Genetic susceptibility has a more important role in pediatric-onset Crohn's disease than in adult-onset Crohn's disease

Inflamm Bowel Dis. 2007 Sep;13(9):1083-92. doi: 10.1002/ibd.20171.

Abstract

Background: Genetic susceptibility may play a more important role in the etiology of early-onset inflammatory bowel disease (IBD) than in late-onset IBD, and therefore pediatric-onset IBD patients can be expected to have a higher frequency of gene mutations. We aimed to determine genotypes and phenotypes of patients with pediatric-onset IBD, to compare them with those of patients with adult-onset IBD and with controls, and to identify genotype-phenotype associations.

Methods: Polymorphisms R702W, G908R, and 3020insC of CARD15 (caspase activating recruitment domain 15); Asp299Gly and Thr399Ile of TLR4; -207G-->C, 1672C-->T (L503F), rs3792876, rs274551, rs272893, and rs273900 of SLC22A4/5; and 113G-->A as well as rs2289311, rs1270912, and rs2165047 of DLG5 (Drosophila discs large homologue 5) were assessed in 103 pediatric-onset and 696 adult-onset IBD patients. Phenotypic classification was based on disease localization and behavior.

Results: Homozygosity for 3020insC in CARD15 was significantly higher in patients with pediatric-onset Crohn's disease (CD) than in patients with adult-onset CD (4.2% versus 0.6%, 95% confidence interval [CI] 1.2-42.0). Homozygosity for single-nucleotide polymorphism (SNP) rs3792876 in SLC22A4/5 was significantly higher in patients with pediatric-onset CD than in patients with adult-onset CD (6.1% versus 1.1%, P=0.02). Polymorphism 3020insC in CARD15 was associated with ileal involvement (1.9% versus 13.3%, CI 1.0-53.8) and a positive family history (6.1% versus 20%, CI 1.2-9.0). DLG5 SNP rs2165047 was significantly associated with perianal disease (50% versus 21.2%, CI 1.4-4).

Conclusions: Polymorphisms 3020insC in CARD15 and SNP rs3792876 in SLC22A4/5 occurred statistically significantly more often in patients with pediatric-onset CD than in patients with adult-onset CD. Polymorphisms 3020insC in CARD15 and SNP rs2165047 in DLG5 were associated with specific phenotypes in this pediatric-onset CD cohort.

MeSH terms

  • Adolescent
  • Adult
  • Age of Onset*
  • Aged
  • Child
  • Child, Preschool
  • Cohort Studies
  • Crohn Disease / genetics*
  • Female
  • Genetic Predisposition to Disease*
  • Humans
  • Infant
  • Male
  • Membrane Proteins / genetics*
  • Middle Aged
  • Nod2 Signaling Adaptor Protein / genetics*
  • Polymorphism, Genetic
  • Polymorphism, Single Nucleotide
  • Tumor Suppressor Proteins / genetics*

Substances

  • DLG5 protein, human
  • Membrane Proteins
  • NOD2 protein, human
  • Nod2 Signaling Adaptor Protein
  • Tumor Suppressor Proteins