A 6-year-old child with pulmonary arteriovenous malformation (PAVM) of the lower lobe of left lung was successfully treated by left lower lobectomy and the case is reported for its rarity. The exact diagnosis is relatively easy to make by contrast echocardiography and pulmonary angiocardiography, provided the possibility is entertained. Because of recurrent episodes of massive haemoptysis from a single pulmonary lobe, surgical resection was deemed the best curative option to avoid further episodes and recurrence. Published reports detailing coil embolisation therapy for PAVMs are also discussed.