Aberrant expression of the Th2 cytokine IL-21 in Hodgkin lymphoma cells regulates STAT3 signaling and attracts Treg cells via regulation of MIP-3alpha

Blood. 2008 Oct 15;112(8):3339-47. doi: 10.1182/blood-2008-01-134783. Epub 2008 Aug 6.

Abstract

The malignant Hodgkin/Reed-Sternberg (HRS) cells of classical Hodgkin lymphoma (HL) are derived from mature B cells, but have lost a considerable part of the B cell-specific gene expression pattern. Consequences of such a lineage infidelity for lymphoma pathogenesis are currently not defined. Here, we report that HRS cells aberrantly express the common cytokine-receptor gamma-chain (gamma(c)) cytokine IL-21, which is usually restricted to a subset of CD4(+) T cells, and the corresponding IL-21 receptor. We demonstrate that IL-21 activates STAT3 in HRS cells, up-regulates STAT3 target genes, and protects HRS cells from CD95 death receptor-induced apoptosis. Furthermore, IL-21 is involved in up-regulation of the CC chemokine macrophage-inflammatory protein-3alpha (MIP-3alpha) in HRS cells. MIP-3alpha in turn attracts CCR6(+)CD4(+)CD25(+)FoxP3(+)CD127(lo) regulatory T cells toward HRS cells, which might favor their immune escape. Together, these data support the concept that aberrant expression of B lineage-inappropriate genes plays an important role for the biology of HL tumor cells.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • CD4-Positive T-Lymphocytes / metabolism
  • Cell Line, Tumor
  • Cell Lineage
  • Cell Proliferation
  • Chemokine CCL20 / metabolism*
  • Gene Expression Regulation, Neoplastic*
  • Hodgkin Disease / metabolism*
  • Humans
  • Immune System
  • Interleukin-6 / metabolism
  • Interleukins / metabolism*
  • STAT3 Transcription Factor / metabolism*
  • T-Lymphocytes, Regulatory / metabolism*
  • Th2 Cells / metabolism*
  • fas Receptor / biosynthesis

Substances

  • CCL20 protein, human
  • Chemokine CCL20
  • Interleukin-6
  • Interleukins
  • STAT3 Transcription Factor
  • STAT3 protein, human
  • fas Receptor
  • interleukin-21