Idiopathic inflammatory myopathies in childhood: current concepts

Pediatr Clin North Am. 2012 Apr;59(2):365-80. doi: 10.1016/j.pcl.2012.03.006.

Abstract

The juvenile idiopathic inflammatory myopathies are a group of rare, chronic, multisystem, autoimmune diseases associated with muscle weakness. This article reviews practical issues of relevance to pediatricians, including clinical presentation, differential diagnosis, investigation, therapy, and prognosis. The importance of early recognition and specialist involvement is emphasized.

Publication types

  • Review

MeSH terms

  • Adrenal Cortex Hormones / therapeutic use
  • Anti-Inflammatory Agents / therapeutic use
  • Child
  • Diagnosis, Differential
  • Humans
  • Myositis* / diagnosis
  • Myositis* / therapy
  • Physical Therapy Modalities
  • Prognosis
  • Treatment Outcome

Substances

  • Adrenal Cortex Hormones
  • Anti-Inflammatory Agents