Neonatal hemodialysis: effective therapy for the encephalopathy of inborn errors of metabolism

J Pediatr. 1990 Jan;116(1):125-8. doi: 10.1016/s0022-3476(05)81661-0.
No abstract available

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Amino Acid Metabolism, Inborn Errors / complications*
  • Amino Acids, Branched-Chain / metabolism
  • Ammonia / metabolism
  • Argininosuccinate Synthase / deficiency*
  • Brain Diseases, Metabolic / etiology
  • Brain Diseases, Metabolic / therapy*
  • Female
  • Glutamine / metabolism
  • Humans
  • Infant, Newborn
  • Keto Acids / metabolism
  • Ligases / deficiency*
  • Male
  • Maple Syrup Urine Disease / complications*
  • Renal Dialysis*

Substances

  • Amino Acids, Branched-Chain
  • Keto Acids
  • Glutamine
  • Ammonia
  • Ligases
  • Argininosuccinate Synthase