Flightless I is a key regulator of the fibroproliferative process in hypertrophic scarring and a target for a novel antiscarring therapy

Br J Dermatol. 2016 Apr;174(4):786-94. doi: 10.1111/bjd.14263. Epub 2016 Jan 9.

Abstract

Background: Hypertrophic scarring carries a large burden of disease, including disfigurement, pain and disability. There is currently no effective medical treatment to reduce or prevent hypertrophic scarring. Flightless I (Flii), a member of the gelsolin family of actin remodelling proteins, is an important negative regulator of wound repair.

Objectives: The objective of this study was to investigate the role of Flii as a potential regulator of hypertrophic scarring.

Methods: Using human skin samples and an animal model of bleomycin-induced hypertrophic scarring in mice that overexpress or have reduced expression of Flii, we investigated its effect on dermal fibrosis and hypertrophic scarring.

Results: Flii expression was increased in human burns and hypertrophic scars. A similar increase in Flii was observed in hypertrophic scars formed in mice post-treatment with bleomycin. However, Flii-deficient (Flii(+/-) ) mice had reduced scarring in response to bleomycin evidenced by decreased dermal thickness, smaller cross-sectional scar areas, fewer myofibroblasts and a decreased collagen I/III ratio. In contrast, bleomycin-treated Flii-overexpressing mice (Flii(Tg/Tg) ) showed increased scar dermal thickness, larger cross-sectional scar areas, more myofibroblasts and an increased collagen I/III ratio. Injecting developing scars with a Flii neutralizing antibody led to a significant reduction in the size of the scars and a reduction in the collagen I/III ratio.

Conclusions: This study identifies Flii as a profibrotic agent that contributes to excessive scar formation. Reducing its activity using neutralizing antibodies is a promising approach for reducing hypertrophic scarring.

Publication types

  • Comparative Study

MeSH terms

  • Animals
  • Antibiotics, Antineoplastic / toxicity
  • Antibodies, Neutralizing / pharmacology
  • Bleomycin / toxicity
  • Burns / physiopathology
  • Carrier Proteins
  • Cicatrix, Hypertrophic / etiology*
  • Cicatrix, Hypertrophic / prevention & control
  • Collagen / metabolism
  • Cytoskeletal Proteins / deficiency
  • Cytoskeletal Proteins / immunology
  • Cytoskeletal Proteins / physiology*
  • Disease Models, Animal
  • Female
  • Humans
  • Mice, Inbred BALB C
  • Microfilament Proteins / deficiency
  • Microfilament Proteins / immunology
  • Microfilament Proteins / physiology*
  • Myofibroblasts / physiology
  • Receptors, Cytoplasmic and Nuclear / deficiency
  • Receptors, Cytoplasmic and Nuclear / immunology
  • Receptors, Cytoplasmic and Nuclear / physiology*
  • Trans-Activators
  • Transforming Growth Factor beta1 / metabolism

Substances

  • Antibiotics, Antineoplastic
  • Antibodies, Neutralizing
  • Carrier Proteins
  • Cytoskeletal Proteins
  • FLII protein, human
  • FlII protein, mouse
  • Microfilament Proteins
  • Receptors, Cytoplasmic and Nuclear
  • Trans-Activators
  • Transforming Growth Factor beta1
  • Bleomycin
  • Collagen