Hereditary Pancreatic Cancer Syndromes: Providing Care to At-Risk Families

Clin J Oncol Nurs. 2019 Dec 1;23(6):579-582. doi: 10.1188/19.CJON.579-582.

Abstract

Hereditary pancreatic cancer continues to pose challenges to providers, as well as to patients and their families. Pancreatic cancer has a poor prognosis, and individuals with family histories of pancreatic cancer are often motivated to pursue genetic testing. This article reviews various hereditary pancreatic cancer syndromes, as well as pancreatic cancer screening recommendations, options, and limitations.

Keywords: gene mutation; genetic testing; hereditary pancreatic cancer; risk assessment.

Publication types

  • Review

MeSH terms

  • Carcinoma / diagnosis
  • Carcinoma / nursing
  • Carcinoma / therapy*
  • Female
  • Genetic Predisposition to Disease*
  • Humans
  • Life Style
  • Male
  • Pancreatic Neoplasms / diagnosis
  • Pancreatic Neoplasms / genetics
  • Pancreatic Neoplasms / nursing
  • Pancreatic Neoplasms / therapy*
  • Risk Factors

Supplementary concepts

  • Pancreatic carcinoma, familial