Dental Management of Neurofibromatosis Type 1: A Case Report and Literature Review

Fabienne Wotjiuk; Isabelle Hyon; Sylvie Dajean-Trutaud; Zahi Badran; Tony Prud'homme

doi:10.5005/jp-journals-10005-1668

Dental Management of Neurofibromatosis Type 1: A Case Report and Literature Review

Int J Clin Pediatr Dent. 2019 Nov-Dec;12(6):577-581. doi: 10.5005/jp-journals-10005-1668.

Authors

Fabienne Wotjiuk¹, Isabelle Hyon², Sylvie Dajean-Trutaud², Zahi Badran³, Tony Prud'homme⁴

Affiliations

¹ Prosthetic Dentistry Department, CHU/Université Nantes, France.
² Pediatric Dentistry Department, CHU/Université Nantes, France.
³ Periodontology Department, CHU/Université Nantes, France; Faculty of Dentistry, McGill University, Montreal, Canada.
⁴ Pediatric Dentistry Department, CHU/Université Nantes, France; UMR 1246 - SPHERE "Methods in Patient-centered Outcomes and Health Research", Université Nantes et Tours, France.

Abstract

Neurofibromatosis type 1 (NF1) is a clinically heterogeneous neurocutaneous genetic disorder that manifests in the form of coffee-milk spots on the skin, Lish nodules, lentigines on the underarms and on the inguinal region, and neurofibromas. Orofacial manifestations of NF1 are common. Through a review of the literature, bone lesions, orthodontic and dental abnormalities, periodontal manifestations, and caries related to NF1 will be explored. In this study, we present a clinical case of a patient with neurofibroma in the oral cavity and infraocclusion of primary molars, as well as his dental management.

How to cite this article: Wotjiuk F, Hyon I, Dajean-Trutaud S, et al. Dental Management of Neurofibromatosis Type 1: A Case Report and Literature Review. Int J Clin Pediatr Dent 2019;12(6):577-581.

Keywords: Dental care; Neurofibromatosis type 1; Oral manifestation.

Publication types

Case Reports