No abstract available
Publication types
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Comparative Study
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Letter
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Observational Study
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Research Support, Non-U.S. Gov't
MeSH terms
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Adolescent
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Adult
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Aminophenols / pharmacology
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Aminophenols / therapeutic use*
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Aminopyridines / pharmacology
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Aminopyridines / therapeutic use*
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Benzodioxoles / pharmacology
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Benzodioxoles / therapeutic use*
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Child
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Chlorides / analysis
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Colforsin
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Cystic Fibrosis / drug therapy*
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Cystic Fibrosis / genetics
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Cystic Fibrosis / physiopathology
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Cystic Fibrosis Transmembrane Conductance Regulator / genetics
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Drug Combinations
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Edema
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Female
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Forced Expiratory Volume
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Homozygote
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Humans
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In Vitro Techniques
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Male
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Membrane Potentials / physiology
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Middle Aged
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Nasal Mucosa / physiopathology
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Organoids / drug effects*
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Precision Medicine
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Prospective Studies
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Quinolones / pharmacology
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Quinolones / therapeutic use*
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Rectum / drug effects*
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Sweat / chemistry
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Treatment Outcome
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Vital Capacity
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Young Adult
Substances
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Aminophenols
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Aminopyridines
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Benzodioxoles
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CFTR protein, human
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Chlorides
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Drug Combinations
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Quinolones
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lumacaftor, ivacaftor drug combination
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Cystic Fibrosis Transmembrane Conductance Regulator
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Colforsin