Lysobisphosphatidic acid (LBPA) enrichment promotes cholesterol egress via exosomes in Niemann Pick type C1 deficient cells

Biochim Biophys Acta Mol Cell Biol Lipids. 2021 Jun;1866(6):158916. doi: 10.1016/j.bbalip.2021.158916. Epub 2021 Mar 12.
No abstract available

Keywords: Bis(monoacylglycero)phosphate; Cholesterol; Exosomes; Extracellular vesicles; Lysobisphosphatidic acid; Niemann-Pick C disease; Phosphatidylglycerol.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Biological Transport / drug effects
  • Cell Line
  • Cholesterol / metabolism*
  • Exosomes / drug effects*
  • Exosomes / metabolism*
  • Humans
  • Lysophospholipids / pharmacology*
  • Monoglycerides / pharmacology*
  • Niemann-Pick C1 Protein / deficiency*

Substances

  • Lysophospholipids
  • Monoglycerides
  • Niemann-Pick C1 Protein
  • bis(monoacylglyceryl)phosphate
  • Cholesterol