Abstract
Segmental spinal dysgenesis is a rare form of spinal dysraphism. We report a case of segmental hypoplasia of the spinal cord extending from T6 to L1 vertebral levels, with a dorsal dermal sinus, diagnosed by spinal sonography and MRI and confirmed at surgery. The probable pathogenesis is suggested.
MeSH terms
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Diagnosis, Differential
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Diagnostic Imaging*
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Female
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Humans
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Infant
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Neurologic Examination
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Spina Bifida Occulta / diagnosis*
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Spina Bifida Occulta / surgery
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Spinal Cord / abnormalities*
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Spinal Cord / pathology
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Spinal Cord / surgery
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Spinal Dysraphism / diagnosis*
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Spinal Dysraphism / surgery
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Spinal Nerve Roots / abnormalities
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Spinal Nerve Roots / pathology
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Spinal Nerve Roots / surgery