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Tafazzin deficiency impairs CoA-dependent oxidative metabolism in cardiac mitochondria.
J Biol Chem. 2020 Aug 28;295(35):12485-12497. doi: 10.1074/jbc.RA119.011229. Epub 2020 Jul 14.
J Biol Chem. 2020.
PMID: 32665401
Free PMC article.
Long-chain fatty acid oxidation and respiratory complex I deficiencies distinguish Barth Syndrome from idiopathic pediatric cardiomyopathy.
Chatfield KC, Sparagna GC, Specht KS, Whitcomb LA, Omar AK, Miyamoto SD, Wolfe LM, Chicco AJ.
Chatfield KC, et al. Among authors: specht ks.
J Inherit Metab Dis. 2022 Jan;45(1):111-124. doi: 10.1002/jimd.12459. Epub 2021 Dec 7.
J Inherit Metab Dis. 2022.
PMID: 34821394
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High-Repetition-Rate Transient Absorption Spectroscopy of Respiratory Supercomplexes.
Wang E, Specht KS, Chicco AJ, Wilson JW.
Wang E, et al. Among authors: specht ks.
J Phys Chem B. 2022 Feb 24;126(7):1404-1412. doi: 10.1021/acs.jpcb.1c08714. Epub 2022 Feb 15.
J Phys Chem B. 2022.
PMID: 35166549
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Nox4 mediates skeletal muscle metabolic responses to exercise.
Specht KS, Kant S, Addington AK, McMillan RP, Hulver MW, Learnard H, Campbell M, Donnelly SR, Caliz AD, Pei Y, Reif MM, Bond JM, DeMarco A, Craige B, Keaney JF Jr, Craige SM.
Specht KS, et al.
Mol Metab. 2021 Mar;45:101160. doi: 10.1016/j.molmet.2020.101160. Epub 2021 Jan 2.
Mol Metab. 2021.
PMID: 33400973
Free PMC article.
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Sensing local energetics to acutely regulate mitophagy in skeletal muscle.
Nichenko AS, Specht KS, Craige SM, Drake JC.
Nichenko AS, et al. Among authors: specht ks.
Front Cell Dev Biol. 2022 Aug 29;10:987317. doi: 10.3389/fcell.2022.987317. eCollection 2022.
Front Cell Dev Biol. 2022.
PMID: 36105350
Free PMC article.
Review.
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Neuromuscular Dysfunction Precedes Cognitive Impairment in a Mouse Model of Alzheimer's Disease.
Brisendine MH, Nichenko AS, Bandara AB, Willoughby OS, Amiri N, Weingrad Z, Specht KS, Bond JM, Addington A, Jones RG 3rd, Murach KA, Poelzing S, Craige SM, Grange RW, Drake JC.
Brisendine MH, et al. Among authors: specht ks.
Function (Oxf). 2023 Dec 4;5(1):zqad066. doi: 10.1093/function/zqad066. eCollection 2024.
Function (Oxf). 2023.
PMID: 38111538
Free PMC article.
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