Background: : Giant congenital melanocytic nevi are rare lesions with the potential to regress into malignant melanoma and/or neurocutaneous melanosis. Appropriate investigations include a screening magnetic resonance imaging scan, neurologic evaluation, and serial clinical observations looking for the development of these complications. Numerous excisional and nonexcisional options have been described for the management of giant congenital melanocytic nevi.
Methods: : A MEDLINE search was performed to obtain all relevant citations.
Conclusions: : To successfully treat these complex lesions, the plastic surgeon must understand the disease process, the natural history and complications, and the options for treatment.