No abstract available
MeSH terms
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Acetylglucosaminidase / deficiency*
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Acetylglucosaminidase / metabolism
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Adolescent
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Brain / metabolism*
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Female
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Glycosaminoglycans / metabolism*
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Glycoside Hydrolases / metabolism
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Hexosaminidases / deficiency*
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Humans
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Lipid Metabolism*
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Liver / metabolism
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Lysosomes / enzymology*
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Mucopolysaccharidoses / metabolism*
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Mucopolysaccharidosis III / metabolism*
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Spleen / metabolism
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Tissue Distribution
Substances
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Glycosaminoglycans
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Glycoside Hydrolases
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Hexosaminidases
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Acetylglucosaminidase