Acute abdominal pain as a leading symptom for Degos' disease (malignant atrophic papulosis)

Am J Gastroenterol. 1999 Apr;94(4):1098-9. doi: 10.1111/j.1572-0241.1999.1022_a.x.


We report a case of a 16-yr-old white female patient with acute abdominal pain due to visceral involvement of Degos' disease that required extensive small bowel resection. Skin manifestations of her disease had been present for 2 yr before the correct diagnosis. She died as a result of central nervous system involvement from Degos' disease.

Publication types

  • Case Reports

MeSH terms

  • Abdomen, Acute / etiology*
  • Adolescent
  • Central Nervous System Diseases / etiology
  • Fatal Outcome
  • Female
  • Humans
  • Intestinal Diseases / etiology*
  • Intestinal Diseases / surgery
  • Skin Diseases, Papulosquamous / complications*
  • Skin Diseases, Vascular / complications*