Liposarcomas are very rare malignancies in the larynx. At present only a few case reports have been described in the available literature. These cases have been highly differentiated liposarcomas, just like our case. The unremarkable clinical picture of these tumors is that of a soft, lipomatous, smooth limited tumor. Findings first appear to be consistent with a lipoma and not a malignancy. Our case of a 23-year-old man is the youngest patient with a laryngeal liposarcoma described thus far. We discuss the surgical procedure used, especially in view of a local recurrence rate of approximately 60%, as well as additional radiotherapy. The treatment of choice is extensive local tumor resection. Chemotherapy is presently not useful for highly differentiated liposarcomas.