Childhood dermatitis herpetiformis: an unusual presentation

Clin Exp Dermatol. 1999 Jul;24(4):283-5. doi: 10.1046/j.1365-2230.1999.00481.x.

Abstract

Childhood dermatitis herpetiformis (DH) is rare. The true prevalence and incidence of this condition are unknown. We report a 7-year-old boy presenting with nonpruritic inflammatory papules on the buttocks and extensor surfaces, clinico-pathologically consistent with Sweet's neutrophilic dermatosis. Immunofluorescence studies showed IgA deposits in the dermal papillae consistent with DH. Remission was achieved with a gluten-free diet and dapsone. Childhood DH may present different clinical signs to the adult form and misdiagnosis can occur if immunofluorescence is not requested on skin biopsy.

Publication types

  • Case Reports

MeSH terms

  • Anti-Inflammatory Agents, Non-Steroidal / therapeutic use
  • Child
  • Dapsone / therapeutic use
  • Dermatitis Herpetiformis / diagnosis*
  • Dermatitis Herpetiformis / pathology
  • Diagnosis, Differential
  • Diet, Protein-Restricted
  • Dietary Proteins / administration & dosage
  • Fluorescent Antibody Technique, Direct
  • Glutens / administration & dosage
  • Humans
  • Immunoglobulin A / analysis
  • Male
  • Skin / pathology
  • Sweet Syndrome / diagnosis

Substances

  • Anti-Inflammatory Agents, Non-Steroidal
  • Dietary Proteins
  • Immunoglobulin A
  • Glutens
  • Dapsone