Congenital pulmonary venous stenosis presenting as persistent pulmonary hypertension of the newborn

Pediatr Pulmonol. 1999 Oct;28(4):301-6. doi: 10.1002/(sici)1099-0496(199910)28:4<301::aid-ppul10>3.0.co;2-m.

Abstract

Congenital pulmonary venous stenosis (CPVS) has been previously described in older infants and children, typically manifesting as failure to thrive with congestive heart failure and subsequent respiratory deterioration. We report on 2 cases of CPVS which presented during the immediate newborn period as severe persistent pulmonary hypertension of the newborn.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Angiography
  • Cardiac Catheterization
  • Constriction, Pathologic / congenital
  • Constriction, Pathologic / diagnosis
  • Diagnosis, Differential
  • Fatal Outcome
  • Female
  • Heart Defects, Congenital / diagnosis*
  • Heart Defects, Congenital / physiopathology
  • Heart Defects, Congenital / therapy
  • Humans
  • Infant, Newborn
  • Male
  • Persistent Fetal Circulation Syndrome / diagnosis*
  • Persistent Fetal Circulation Syndrome / physiopathology
  • Persistent Fetal Circulation Syndrome / therapy
  • Pulmonary Veins / abnormalities*
  • Respiration, Artificial