Right heart failure as the dominant clinical picture in a case of primary amyloidosis affecting the pulmonary vasculature

Scott Med J. 1999 Aug;44(4):116-7. doi: 10.1177/003693309904400407.


A 91-year-old female patient died of right heart failure and pulmonary hypertension. The autopsy revealed multi-organ vascular amyloidosis and pulmonary alveolar septal amyloidosis with no evidence of parenchymal myocardial amyloid deposition. This is a rare example of cor pulmonale secondary to pulmonary amyloidosis.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Aged, 80 and over
  • Amyloidosis / complications*
  • Amyloidosis / pathology*
  • Fatal Outcome
  • Female
  • Humans
  • Hypertension, Pulmonary / complications*
  • Pulmonary Heart Disease / etiology*
  • Pulmonary Heart Disease / pathology
  • Ventricular Dysfunction, Right / pathology*