Bile acid synthetic defects and liver disease

Pediatr Dev Pathol. 2000 Jan-Feb;3(1):1-16. doi: 10.1007/s100240050001.
No abstract available

Publication types

  • Review

MeSH terms

  • 3-Hydroxysteroid Dehydrogenases / deficiency
  • Animals
  • Bile Acids and Salts / biosynthesis*
  • Cytochrome P-450 Enzyme System / deficiency
  • Cytochrome P450 Family 7
  • Humans
  • Liver Diseases / enzymology
  • Liver Diseases / physiopathology*
  • Models, Biological
  • Steroid Hydroxylases / deficiency
  • Steroid Isomerases / deficiency
  • Zellweger Syndrome / enzymology
  • Zellweger Syndrome / physiopathology

Substances

  • Bile Acids and Salts
  • Cytochrome P-450 Enzyme System
  • 3-Hydroxysteroid Dehydrogenases
  • Steroid Hydroxylases
  • oxysterol 7-alpha-hydroxylase
  • Cytochrome P450 Family 7
  • CYP7B1 protein, human
  • Steroid Isomerases
  • steroid delta-isomerase