Microangiopathy of the inner ear, retina, and brain (Susac syndrome): report of a case

Arch Otolaryngol Head Neck Surg. 2000 Jan;126(1):82-4. doi: 10.1001/archotol.126.1.82.


Microangiopathy of the inner ear, retina, and brain was first described in 1979 by John O. Susac. Since then, approximately 60 cases have been reported. Otolaryngologists must be aware of this syndrome, in which cochleovestibular symptoms are an important part of the diagnosis. In this article, we report a new case of Susac syndrome and discuss the diagnosis, physiopathologic characteristics, and treatment of this disease.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Audiometry, Pure-Tone
  • Brain / pathology
  • Brain Diseases / pathology*
  • Female
  • Hearing Loss, Sensorineural / pathology*
  • Humans
  • Magnetic Resonance Imaging
  • Microcirculation
  • Retinal Artery Occlusion / pathology*
  • Syndrome