Pre-excitation syndrome secondary to cardiac rhabdomyomas in tuberous sclerosis

J Paediatr Child Health. 2000 Feb;36(1):84-6. doi: 10.1046/j.1440-1754.2000.00443.x.


Rhabdomyomas are not uncommon in infants with tuberous sclerosis. We describe a neonate who presented with hydrops fetalis arising from a tachyarrhythmia during fetal life related to rhabdomyomas. After reversion of the arrhythmia, pre-excitation was noted on an interval electrocardiogram. Following regression of the tumours, the delta wave disappeared with no further arrhythmias noted.

Publication types

  • Case Reports

MeSH terms

  • Cesarean Section
  • Electrocardiography
  • Female
  • Fetal Diseases / diagnosis
  • Heart Neoplasms / complications*
  • Heart Neoplasms / diagnostic imaging
  • Humans
  • Hydrops Fetalis / diagnostic imaging
  • Infant, Newborn
  • Pre-Excitation Syndromes / etiology*
  • Pregnancy
  • Rhabdomyoma / complications*
  • Rhabdomyoma / diagnostic imaging
  • Tachycardia / etiology
  • Tuberous Sclerosis / complications*
  • Tuberous Sclerosis / diagnosis
  • Ultrasonography, Prenatal