Bilateral optic neuropathy associated with diffuse cerebral angiomatosis in Sturge-Weber syndrome

J Neuroophthalmol. 2000 Mar;20(1):28-31. doi: 10.1097/00041327-200020010-00010.


Visual loss in patients with encephalotrigeminal angiomatosis or Sturge-Weber syndrome usually results from secondary glaucoma or from damage to the retrogeniculate pathways by the angiomatous lesions. Optic neuropathy has not been reported as a component of this syndrome. This report describes a patient who developed bilateral optic neuropathy with progressive visual loss associated with diffuse cerebral angiomatosis in the setting of Sturge-Weber syndrome.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Angiomatosis / complications
  • Biopsy
  • Blindness / etiology*
  • Brain Diseases / complications*
  • Brain Diseases / pathology
  • Female
  • Frontal Lobe / pathology
  • Humans
  • Magnetic Resonance Imaging
  • Optic Disk / pathology
  • Optic Nerve Diseases / etiology*
  • Sturge-Weber Syndrome / complications*
  • Sturge-Weber Syndrome / pathology
  • Visual Acuity
  • Visual Fields