Abstract
We present the unique case of a 2-year-old girl with congenital athyreosis who acquired primary measles virus infection at the age of 18 months, coincidentally with an Epstein-Barr virus infection. First neurologic symptoms of subacute sclerosing panencephalitis appeared 5 months later, and the girl died within 6 months after a rapid progressive illness. Factors possibly predisposing to this extraordinary disease course-primary measles virus infection at an early age and lack of evidence for immunodeficiency-are discussed.
MeSH terms
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Brain / pathology
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Child, Preschool
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Chorioretinitis / immunology
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Chorioretinitis / pathology
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Chorioretinitis / virology
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Epstein-Barr Virus Infections / complications*
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Epstein-Barr Virus Infections / virology
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Eye / pathology
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Female
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Humans
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Magnetic Resonance Imaging / methods
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Measles / complications*
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Measles / virology
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Subacute Sclerosing Panencephalitis / complications*
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Subacute Sclerosing Panencephalitis / diagnosis
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Subacute Sclerosing Panencephalitis / immunology
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Subacute Sclerosing Panencephalitis / virology
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Thyroid Gland / abnormalities*
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Time Factors