[Anesthetic management of a patient with Freeman-Sheldon syndrome]

Masui. 2000 Aug;49(8):901-2.
[Article in Japanese]


We describe a case of Freeman-Sheldon syndrome that presented some problems for anesthetic management. A 2-yr-old girl required orthopedic surgery for the bilateral lower extremities. Anesthesia was induced via a mask with oxygen (2 l.min-1), nitrous oxide (4 l.min-1) and sevoflurane (approximately 5%). Tracheal intubation by direct laryngoscopy was successfully achieved. Combined caudal epidural block was, however, avoided because spina bifida occulta was suspected. Spina bifida occulta was revealed postoperatively by X-ray. For anesthetic management of a patient with Freeman-Sheldon syndrome, the spine should be evaluated preoperatively when performing epidural/spinal anesthesia.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple*
  • Anesthesia, Epidural
  • Anesthesia, Inhalation*
  • Anesthesia, Spinal
  • Child, Preschool
  • Contraindications
  • Craniofacial Abnormalities*
  • Female
  • Foot Deformities / surgery*
  • Hand Deformities
  • Humans
  • Intubation, Intratracheal / methods
  • Muscular Diseases
  • Orthopedic Procedures
  • Spinal Dysraphism / complications
  • Syndrome