Anaesthetic management of children with congenital insensitivity to pain with anhidrosis

Paediatr Anaesth. 2000;10(5):545-8. doi: 10.1046/j.1460-9592.2000.00542.x.

Abstract

Congenital insensitivity to pain with anhidrosis (CIPA) is a rare sensory neuropathy, which affects patients' pain sensation and thermoregulation. There are several issues to consider when planning anaesthesia for those with this congenital disorder. Over a 20-year period, six patients with CIPA underwent 20 surgical procedures under general anaesthesia in our institution. We analysed our experience with these patients retrospectively. We conclude that patients with CIPA are able to undergo surgical procedures under general anaesthesia without major problems.

Publication types

  • Clinical Trial

MeSH terms

  • Adolescent
  • Anesthesia, General*
  • Body Temperature Regulation / physiology
  • Child
  • Child, Preschool
  • Female
  • Humans
  • Hypohidrosis / complications*
  • Hypohidrosis / physiopathology
  • Male
  • Pain Insensitivity, Congenital / complications*
  • Pain Insensitivity, Congenital / physiopathology
  • Retrospective Studies