Treatment of spontaneous carotid-cavernous fistula in Ehlers-Danlos syndrome by transvenous occlusion with Guglielmi detachable coils. Case report and review of the literature

J Neurosurg. 2000 Oct;93(4):689-92. doi: 10.3171/jns.2000.93.4.0689.


The authors report on a young woman with Ehlers-Danlos syndrome (EDS) Type IV in whom a spontaneous direct carotid-cavernous fistula (CCF) was treated by transvenous occlusion with regular and fiber-coated Guglielmi detachable coils. To the authors' knowledge, this is the first time this approach has been used in a patient with EDS. The different treatment options are discussed, and the literature on endovascular treatment of direct CCFs in EDS is reviewed.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Carotid-Cavernous Sinus Fistula / etiology
  • Carotid-Cavernous Sinus Fistula / therapy*
  • Cerebral Angiography
  • Ehlers-Danlos Syndrome / complications*
  • Embolization, Therapeutic / instrumentation*
  • Embolization, Therapeutic / methods
  • Female
  • Humans
  • Stents
  • Treatment Outcome