Background: Pseudo-doubling of the optic nerve head is a spectacular clinical entity, in which a lesion resembling an optic disk appears adjacent to the true optic disk.
Case report: A case of unilateral pseudo-doubling of the optic disk with bilateral optic nerve pits is presented.
Conclusions: The lesion is congenital, and represents a chorioretinal coloboma with optic disk involvement. Pseudo-doubling can be differentiated from true doubling of the optic nerve by the imaging techniques of ultrasonography, computerized tomography, and magnetic resonance imaging.