Progressive facial hemiatrophy after epileptic seizures

Pediatr Neurol. 2000 Aug;23(2):164-6. doi: 10.1016/s0887-8994(00)00168-5.


Intractable complex partial seizures developed in a 3-year-old female with normal intracranial findings on computed tomography. Frontal paramedian band-like depression of the skin gradually developed thereafter, and progressive facial hemiatrophy (Parry-Romberg syndrome) was diagnosed. Computed tomography scanning at 5 years of age revealed multiple parenchymal calcifications and low-density areas in the white matter of the frontoparietal lobes. Epileptic seizures, one of the major neurologic complications of progressive facial hemiatrophy, could precede the succeeding neurocutaneous changes.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Electroencephalography
  • Epilepsy / complications
  • Epilepsy / diagnosis*
  • Facial Hemiatrophy / complications
  • Facial Hemiatrophy / diagnosis*
  • Facial Hemiatrophy / physiopathology
  • Female
  • Humans
  • Magnetic Resonance Imaging