Moyamoya syndrome after radiation therapy for optic pathway glioma: case report

J Child Neurol. 2000 Nov;15(11):765-7. doi: 10.1177/088307380001501112.

Abstract

We present a 4-year-old girl with neurofibromatosis-1 who developed moyamoya syndrome characterized by bilateral stenosis or occlusion of the distal internal carotid arteries and their branches, leading to the development of an abnormal vascular network. In light of a literature review, the postradiation vasculopathy of the moyamoya type and its relationship with neurofibromatosis-1 are discussed.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Abnormalities, Radiation-Induced* / diagnostic imaging
  • Abnormalities, Radiation-Induced* / physiopathology
  • Age Factors
  • Cerebrovascular Circulation
  • Child, Preschool
  • Female
  • Humans
  • Magnetic Resonance Angiography
  • Moyamoya Disease / diagnostic imaging
  • Moyamoya Disease / etiology*
  • Moyamoya Disease / physiopathology
  • Neurofibromatosis 1 / complications*
  • Neurofibromatosis 1 / physiopathology
  • Optic Nerve Glioma / etiology
  • Optic Nerve Glioma / radiotherapy*
  • Radiography