No abstract available
MeSH terms
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3-Hydroxysteroid Dehydrogenases / deficiency*
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Adult
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Chenodeoxycholic Acid / therapeutic use
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Cholic Acid / therapeutic use
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Female
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Humans
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Liver / pathology
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Liver Cirrhosis / diagnosis
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Liver Cirrhosis / etiology*
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Metabolism, Inborn Errors / complications
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Metabolism, Inborn Errors / diagnosis
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Metabolism, Inborn Errors / drug therapy
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Steroid Isomerases / deficiency
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Ursodeoxycholic Acid / therapeutic use
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Vitamin K Deficiency / diagnosis
Substances
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Chenodeoxycholic Acid
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Ursodeoxycholic Acid
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3-Hydroxysteroid Dehydrogenases
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Steroid Isomerases
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Cholic Acid