Right pulmonary artery sarcoma

Pathology. 2001 May;33(2):243-5. doi: 10.1080/00313020120038593.


A 57-year-old man presented with cough, chest pain and dyspnea. Peripheral lung opacities detected radiologically on admission were surgically resected and histologically confirmed as pulmonary infarcts. Subsequent radiological examinations revealed a stricture of the right pulmonary artery with evidence of pulmonary hypertension. The patient was commenced on anticoagulant therapy, which resulted in some clinical improvement. A hilar mass detected later was resected together with the right lung. Pathological examination of the hilar mass revealed a tumour within the lumen of the pulmonary artery causing almost total occlusion of the artery. Histology showed angiosarcomatous and osteosarcomatous areas. The patient is well and disease-free 9 months following resection.

Publication types

  • Case Reports

MeSH terms

  • Disease-Free Survival
  • Hemangiosarcoma / diagnostic imaging
  • Hemangiosarcoma / pathology*
  • Hemangiosarcoma / surgery
  • Humans
  • Male
  • Middle Aged
  • Osteosarcoma / pathology
  • Pulmonary Artery / diagnostic imaging
  • Pulmonary Artery / pathology*
  • Pulmonary Artery / surgery
  • Tomography, X-Ray Computed
  • Treatment Outcome
  • Vascular Neoplasms / diagnostic imaging
  • Vascular Neoplasms / pathology*
  • Vascular Neoplasms / surgery