Living-donor lobar lung transplantation for primary ciliary dyskinesia

Ann Thorac Surg. 2001 Jun;71(6):2008-9. doi: 10.1016/s0003-4975(00)02276-1.


A ventilator-dependent patient with primary ciliary dyskinesia underwent successful living-donor lobar lung transplantation. The case was a 24-year-old woman who had developed recurrent lower respiratory infection and became ventilator-dependent due to severe bronchiectasis. Transmission electron microscopy of the resected bronchus demonstrated inner dynein arm deficiency.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Bronchiectasis / pathology
  • Bronchiectasis / surgery
  • Cilia / pathology
  • Ciliary Motility Disorders / pathology
  • Ciliary Motility Disorders / surgery*
  • Dyneins / deficiency
  • Female
  • Humans
  • Living Donors*
  • Lung Transplantation / pathology*
  • Microscopy, Electron


  • Dyneins