Pseudo-maple syrup urine disease due to maternal prenatal ingestion of fenugreek

S H Korman; E Cohen; A Preminger

doi:10.1046/j.1440-1754.2001.00617.x

Pseudo-maple syrup urine disease due to maternal prenatal ingestion of fenugreek

J Paediatr Child Health. 2001 Aug;37(4):403-4. doi: 10.1046/j.1440-1754.2001.00617.x.

Authors

S H Korman¹, E Cohen, A Preminger

Affiliation

¹ Departments of Clinical Biochemistry, Hadassah University Hospital, Jerusalem, Israel. korman@hadassah.org.il

PMID: 11532065
DOI: 10.1046/j.1440-1754.2001.00617.x

Abstract

Fenugreek, maple syrup and the urine of maple syrup urine disease (MSUD) patients all share a characteristic odour originating from a common component, sotolone. Ingestion of fenugreek by mothers during labour resulted in a maple syrup-like odour in their newborn infants, leading to a false suspicion of MSUD.

Publication types

Case Reports

MeSH terms

Diagnostic Errors
Female
Humans
Infant, Newborn
Male
Maple Syrup Urine Disease / diagnosis*
Maternal-Fetal Exchange
Medicine, Traditional
Plant Extracts / pharmacology*
Pregnancy
Trigonella

Substances

Plant Extracts
fenugreek seed meal