Pseudotumour cerebri occurring in association with the Chiari malformation

J Clin Neurosci. 2002 Jan;9(1):99-101. doi: 10.1054/jocn.2000.0947.


Summary The case is described of a 12-year-old girl presenting with raised intracranial pressure without ventricular dilatation and a type 1 Chiari malformation. This was taken to be a coincidental association of pseudotumour cerebri and the Chiari malformation. Treatment of the pseudotumour with Diamox gave rapid and sustained relief of the intracranial hypertension without change in the Chiari malformation. In addition, a series of 156 cases of pseudotumour cerebri was reviewed for evidence of the Chiari malf ormation. An overall incidence of 1.3%, rising to 2.7% in patients with MR scanning [excluding the case described] was found.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acetazolamide / therapeutic use
  • Arnold-Chiari Malformation / complications*
  • Arnold-Chiari Malformation / diagnosis
  • Child
  • Female
  • Humans
  • Magnetic Resonance Imaging
  • Pseudotumor Cerebri / complications*
  • Pseudotumor Cerebri / drug therapy


  • Acetazolamide