Formation of pannus on prosthetic valves in a child with pseudoxanthoma elasticum

Cardiol Young. 2002 Mar;12(2):183-5. doi: 10.1017/s1047951102000380.

Abstract

A child with pseudoxanthoma elasticum had mitral valvar prolapse with severe regurgitation necessitating replacement with a prosthetic valve. Extensive formation of pannus caused obstruction of two mechanical valves, one after twenty months and the second after three years. Histology of the pannus was similar to the endocardial lesions that are considered unique to pseudoxanthoma elasticum.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Female
  • Follow-Up Studies
  • Heart Valve Prosthesis Implantation / adverse effects
  • Heart Valve Prosthesis*
  • Humans
  • Mitral Valve Insufficiency / complications*
  • Mitral Valve Insufficiency / congenital
  • Mitral Valve Insufficiency / diagnostic imaging
  • Mitral Valve Insufficiency / surgery*
  • Prosthesis Design
  • Prosthesis Failure*
  • Pseudoxanthoma Elasticum / complications*
  • Pseudoxanthoma Elasticum / diagnosis
  • Reoperation
  • Risk Assessment
  • Severity of Illness Index
  • Ultrasonography