Orbital lipomatous haemangiopericytoma: an unusual variant

Clin Exp Ophthalmol. 2002 Aug;30(4):281-3. doi: 10.1046/j.1442-9071.2002.00542.x.


Haemangiopericytoma (HPC) of the orbit is a rare tumour occurring in all age groups and presenting with slowly progressive proptosis, ocular motility impairment and visual loss. Although most are benign tumours that are resectable at diagnosis, one-third of these tumours demonstrate malignant features and recur locally or metastasize, usually with a fatal outcome. In 1995, a morphologically unique variant, termed lipomatous haemangiopericytoma (L-HPC), was described. Only one case has been reported previously arising in the orbit. In this paper, a case is reported of L-HPC occurring in the orbit and consider the prognostic implications of this HPC variant.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Diplopia / diagnosis
  • Exophthalmos / diagnosis
  • Hemangiopericytoma / diagnostic imaging
  • Hemangiopericytoma / pathology*
  • Hemangiopericytoma / surgery
  • Humans
  • Lipomatosis / diagnostic imaging
  • Lipomatosis / pathology*
  • Lipomatosis / surgery
  • Male
  • Orbital Neoplasms / diagnostic imaging
  • Orbital Neoplasms / pathology*
  • Orbital Neoplasms / surgery
  • Tomography, X-Ray Computed
  • Visual Acuity