Chenodeoxycholic acid inhibits increased cholesterol and cholestanol synthesis in patients with cerebrotendinous xanthomatosis

Biochem Med. 1975 Sep;14(1):57-74. doi: 10.1016/0006-2944(75)90020-4.
No abstract available

Publication types

  • Research Support, U.S. Gov't, Non-P.H.S.
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Achilles Tendon / metabolism*
  • Adult
  • Alcohols / metabolism
  • Bile / drug effects
  • Bile / metabolism
  • Bile Acids and Salts / metabolism
  • Chenodeoxycholic Acid / pharmacology*
  • Cholesterol / metabolism*
  • Female
  • Humans
  • Hydroxymethylglutaryl CoA Reductases / metabolism
  • Liver / drug effects
  • Liver / enzymology
  • Male
  • Middle Aged
  • Muscular Diseases / metabolism*
  • Sterols / metabolism*
  • Xanthomatosis / metabolism*

Substances

  • Alcohols
  • Bile Acids and Salts
  • Sterols
  • Chenodeoxycholic Acid
  • Cholesterol
  • Hydroxymethylglutaryl CoA Reductases