Phosphatidylinositol 3-kinase/Akt pathway regulates tuberous sclerosis tumor suppressor complex by phosphorylation of tuberin

J Biol Chem. 2002 Sep 20;277(38):35364-70. doi: 10.1074/jbc.M205838200. Epub 2002 Jul 11.

Abstract

Normal cellular functions of hamartin and tuberin, encoded by the TSC1 and TSC2 tumor suppressor genes, are closely related to their direct interactions. However, the regulation of the hamartin-tuberin complex in the context of the physiologic role as tumor suppressor genes has not been documented. Here we show that insulin or insulin growth factor (IGF) 1 stimulates phosphorylation of tuberin, which is inhibited by the phosphatidylinositol 3-kinase (PI3K) inhibitor LY294002 but not by the mitogen-activated protein kinase inhibitor PD98059. Expression of constitutively active PI3K or active Akt, including Akt1 and Akt2, induces tuberin phosphorylation. We further demonstrate that Akt/PKB associates with hamartin-tuberin complexes, promoting phosphorylation of tuberin and increased degradation of hamartin-tuberin complexes. The ability to form complexes, however, is not blocked. Akt also inhibits tuberin-mediated degradation of p27(kip1), thereby promoting CDK2 activity and cellular proliferation. Our results indicate that tuberin is a direct physiological substrate of Akt and that phosphorylation of tuberin by PI3K/Akt is a major mechanism controlling hamartin-tuberin function.

Publication types

  • Research Support, U.S. Gov't, Non-P.H.S.
  • Research Support, U.S. Gov't, P.H.S.
  • Retracted Publication

MeSH terms

  • Amino Acid Sequence
  • Animals
  • Blood
  • Cell Line
  • Genes, Tumor Suppressor*
  • Humans
  • Hydrolysis
  • Insulin / metabolism
  • Insulin-Like Growth Factor I / metabolism
  • Phosphatidylinositol 3-Kinases / metabolism*
  • Phosphorylation
  • Protein Serine-Threonine Kinases / metabolism*
  • Proteins / genetics*
  • Proteins / metabolism
  • Proto-Oncogene Proteins / metabolism*
  • Proto-Oncogene Proteins c-akt
  • Rats
  • Repressor Proteins / genetics*
  • Repressor Proteins / metabolism*
  • Substrate Specificity
  • Tuberous Sclerosis Complex 1 Protein
  • Tuberous Sclerosis Complex 2 Protein
  • Tumor Suppressor Proteins

Substances

  • Insulin
  • Proteins
  • Proto-Oncogene Proteins
  • Repressor Proteins
  • TSC1 protein, human
  • TSC2 protein, human
  • Tsc1 protein, rat
  • Tsc2 protein, rat
  • Tuberous Sclerosis Complex 1 Protein
  • Tuberous Sclerosis Complex 2 Protein
  • Tumor Suppressor Proteins
  • Insulin-Like Growth Factor I
  • AKT1 protein, human
  • AKT2 protein, human
  • Akt1 protein, rat
  • Akt2 protein, rat
  • Protein Serine-Threonine Kinases
  • Proto-Oncogene Proteins c-akt