Complete thoracic ectopia cordis

Eur J Cardiothorac Surg. 2003 Mar;23(3):426-8. doi: 10.1016/s1010-7940(02)00811-4.


Thoracic ectopia cordis is a rare congenital defect with very few reported survivors after surgical correction. We report a case of complete thoracic ectopia cordis with double outlet right ventricle. The diagnosis was established antenatally and a repair was undertaken soon after birth. The child remained stable and was extubated on the fifth post-operative day. Forty-eight hours later the child succumbed to an unexplained respiratory arrest. Also presented is a review of the different surgical strategies for this unusual condition.

Publication types

  • Case Reports

MeSH terms

  • Cardiac Surgical Procedures / methods
  • Double Outlet Right Ventricle / surgery
  • Fatal Outcome
  • Heart Defects, Congenital / surgery*
  • Humans
  • Infant, Newborn
  • Sternum / abnormalities