Anaesthetic and airway management in a child with Hanhart's syndrome

Paediatr Anaesth. 2003 Mar;13(3):263-6. doi: 10.1046/j.1460-9592.2003.01029.x.

Abstract

Hanhart's syndrome (oromandibular-limb hypogenesis syndrome) is a rare disease characterized by hypoglossia/aglossia, various distal limb defects and micrognathia. Difficult airway due to micrognathia may complicate anaesthetic management in this syndrome. We describe the anaesthetic management of a child with Hanhart's syndrome undergoing plastic reconstructive surgery.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple*
  • Airway Obstruction / complications*
  • Anesthesia, Inhalation*
  • Anesthetics, Inhalation / therapeutic use
  • Child, Preschool
  • Humans
  • Intubation, Intratracheal*
  • Male
  • Methyl Ethers / therapeutic use
  • Microstomia / complications*
  • Mouth Abnormalities / surgery*
  • Nitrous Oxide / therapeutic use
  • Oxygen / therapeutic use
  • Reconstructive Surgical Procedures
  • Sevoflurane
  • Syndrome
  • Tongue / abnormalities

Substances

  • Anesthetics, Inhalation
  • Methyl Ethers
  • Sevoflurane
  • Nitrous Oxide
  • Oxygen