Abstract
Bilateral fetal rhabdomyomatous nephroblastoma is a rare variant of Wilms' Tumor. The authors report the evolution over 48 months of a 10-month-old baby with bilateral nephroblastoma for which a left nephrectomy was initially performed. A right kidney tumor was enucleated preserving the kidney. The transformation of the primary tumor into a completely differentiated cystic nephroblastoma or nephromalike tumor and the appearance of a metachronous lesion was seen. This report emphasizes the role of nephron-sparing surgery in bilateral Wilms' Tumor when a benign transformation occurs under chemotherapy.
Copyright 2003, Elsevier Science (USA). All rights reserved.
MeSH terms
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Antineoplastic Combined Chemotherapy Protocols / administration & dosage
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Antineoplastic Combined Chemotherapy Protocols / pharmacology
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Antineoplastic Combined Chemotherapy Protocols / therapeutic use
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Cell Differentiation / drug effects
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Combined Modality Therapy
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Dactinomycin / administration & dosage
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Dactinomycin / pharmacology
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Female
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Humans
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Infant
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Kidney Neoplasms / drug therapy
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Kidney Neoplasms / pathology
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Kidney Neoplasms / surgery*
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Neoplasms, Multiple Primary / surgery*
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Nephrectomy / methods*
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Remission Induction
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Tomography, X-Ray Computed
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Ultrasonography, Interventional
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Vincristine / administration & dosage
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Vincristine / pharmacology
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Wilms Tumor / drug therapy
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Wilms Tumor / pathology
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Wilms Tumor / surgery*