The Cheshire Cat Syndrome: an unusual case of neurosarcoidosis

Sarcoidosis Vasc Diffuse Lung Dis. 2003 Jun;20(2):149-51.

Abstract

Clinical diagnosis of neurosarcoidosis depends on the finding of neurological disease in a patient with biopsy proven multisystem sarcoidosis. Without the biopsy evidence, solitary central nervous system sarcoidosis remains a difficult diagnosis. In some cases, only a long-term follow-up will establish the diagnosis.

Publication types

  • Case Reports

MeSH terms

  • Adrenal Cortex Hormones / therapeutic use
  • Adult
  • Diagnosis, Differential
  • Facial Nerve Diseases / etiology
  • Female
  • Headache / etiology
  • Humans
  • Magnetic Resonance Imaging
  • Nervous System Diseases / diagnosis*
  • Nervous System Diseases / pathology*
  • Sarcoidosis / diagnosis*
  • Sarcoidosis / pathology*
  • Time Factors

Substances

  • Adrenal Cortex Hormones