Obstetric course and neonatal outcome in women with Marfan syndrome is the aim of numerous analyses. It is well known that pregnancies complicated by Marfan syndrome increase the risk of maternal morbidity and premature mortality. The main cause of this is cardiovascular abnormalities (aortic root dilatation, aortic dissection, rupture of the aorta, other cardiac abnormalities). We have presented a case history of a pregnant woman with a Marfan syndrome and the review of the literature.