Long QT syndrome: novel insights into the mechanisms of cardiac arrhythmias

J Clin Invest. 2003 Sep;112(6):810-5. doi: 10.1172/JCI19844.

Abstract

The congenital long QT syndrome is a rare disorder in which mutation carriers are at risk for polymorphic ventricular tachycardia and/or sudden cardiac death. Discovery and analysis of gene mutations associated with variants of this disorder have provided novel insight into mechanisms of cardiac arrhythmia and have raised the possibility of mutation-specific therapeutic intervention.

Publication types

  • Review

MeSH terms

  • Animals
  • Genotype
  • Heart / physiology
  • Humans
  • Long QT Syndrome / diagnosis
  • Long QT Syndrome / genetics
  • Long QT Syndrome / physiopathology*
  • Long QT Syndrome / therapy
  • Mutation
  • Phenotype
  • Potassium Channels / metabolism
  • Protein Subunits / genetics
  • Protein Subunits / metabolism
  • Signal Transduction / physiology
  • Sodium Channels / genetics
  • Sodium Channels / metabolism*

Substances

  • Potassium Channels
  • Protein Subunits
  • Sodium Channels