Laminar heterotopic grey matter (double cortex) in a patient with late onset Lennox-Gastaut syndrome

Wien Klin Wochenschr. 1992;104(19):607-8.


The Lennox-Gastaut syndrome (LGS) is a severe epileptic disorder, characterized by developmental delay, typical electroencephalographic pattern and poor control of seizures. This epileptic syndrome generally presents in early childhood but exceptionally starts at the age of 5 years or later. We describe a patient who was classified as late-onset LGS, with evidence of mild hydrocephalus on CT. MRI added new diagnostic information by demonstrating laminar heterotopic grey matter.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Brain Neoplasms / complications*
  • Brain Neoplasms / diagnosis
  • Cerebral Cortex*
  • Choristoma / complications*
  • Choristoma / diagnosis
  • Electroencephalography
  • Epilepsy, Absence / etiology*
  • Epilepsy, Generalized / etiology*
  • Epilepsy, Tonic-Clonic / etiology*
  • Female
  • Humans
  • Intellectual Disability / etiology
  • Magnetic Resonance Imaging
  • Tomography, X-Ray Computed