Ampullary carcinoid tumor presenting as acute pancreatitis in a patient with von Recklinghausen's disease: case report and review of the literature

W Mayoral; J Salcedo; F Al-Kawas

doi:10.1055/s-2003-42613

Ampullary carcinoid tumor presenting as acute pancreatitis in a patient with von Recklinghausen's disease: case report and review of the literature

Endoscopy. 2003 Oct;35(10):854-7. doi: 10.1055/s-2003-42613.

Authors

W Mayoral¹, J Salcedo, F Al-Kawas

Affiliation

¹ Division of Gastroenterology, Georgetown University Hospital, Washington, DC 20007, USA.

PMID: 14551865
DOI: 10.1055/s-2003-42613

Abstract

A patient with von Recklinghausen syndrome presented with multiple attacks of pancreatitis. Evaluation using computed tomography, endoscopic retrograde cholangiopancreatography, and endosonography revealed an ampullary carcinoid. The patient underwent a pylorus-sparing Whipple resection, and is doing well after 30 months of follow-up. This is the second reported case of ampullary carcinoid presenting with pancreatitis in a patient with von Recklinghausen syndrome.

Publication types

Case Reports
Review

MeSH terms

Ampulla of Vater*
Carcinoid Tumor / complications*
Carcinoid Tumor / diagnosis
Carcinoid Tumor / pathology
Cholangiopancreatography, Endoscopic Retrograde
Common Bile Duct Neoplasms / complications*
Common Bile Duct Neoplasms / diagnosis
Common Bile Duct Neoplasms / pathology
Female
Humans
Middle Aged
Neurofibromatosis 1 / complications*
Pancreatitis / complications*